Question 105:Which one of the following does not produce cyanosis in the first year of life ?
A) Atrial septal defect
B) Hypoplastic left heart syndrome
C) Truncus arteriosus
D) Double outlet right ventricle
Ans:A
Question 106:The treatment of choice for primary grade V vesicoureteric reflux involving both kidneys in a 6 month old boy is ?
A) Antibiotic prophylaxis
B) Ureteric reimplantation
C) Cystoscopy followed by subureteric injection of teflon
D) Bilateral ureterostomies
Ans:B
Question 107:The recommended treatment for preputial adhesions producing ballooning of prepuce during micturition in a 2 year old boy is ?
A) Wait and watch policy
B) Circumcision
C) Doral slit
D) Preputial adhesions release and dilatation
Ans:D
Question 108:The narrowest part of larynx in infants is at the cricoid level. In administering anaethesia this may lead to all except ?
A) Choosing a smaller size endotracheal tube
B) Trauma to the subglottic region
C) Post operative stridor
D) Laryngeal oedema
Ans:D
Question 109:The most common leukocytoclastic vasculitis affecting children is ?
A) Takayasu disease
B) Mucocutaneous lymph node syndrome (Kawasaki disease)
C) Henoch Schonlein Purpura
D) Polyarteritis nodosa
Ans:C
Question 110:The following statements regarding Turner syndrome are true except ?
A) Occurrence of Turner syndrome is influenced by maternal age
B) Most patients have primary amenorrhoea
C) Most patients have short stature
D) Edema of hands and feet is an important feature during infancy
Ans:A
Question 111:One year old male child is presented with poor urinary stream since birth. The investigation of choice for evaluation is ?
A) Voiding cystourethrography (VCUG)
B) USG bladder
C) Intravenous urography
D) Uroflometry
Ans:A
Question 112:In neonatal screening programme for detection of congenital hypothyroidismm the ideal place and time to collect the blood sample for TSH estimation is ?
A) Cord blood at time of birth
B) Heal pad blood at the time of birth
C) Heal pad blood on 4 day of birth
D) Peripheral venous blood on 28 day
Ans:A
Question 113:Commonest cause of neonatal mortality in India is ?
A) Diarrheal diseases
B) Birth injuries
C) Low birth weight
D) Congenital anomalies
Ans:C
Question 114:All of the following methods are used for the diagnosis of HIV infection in a 2 month old child, except ?
A) DNA-PCR
B) Viral culture
C) HIV ELISA
D) p24 antigen assay
Ans:C
Question 115:All of the following are characterstic features of Kwashiorkor, except ?
A) High blood osmolarity
B) Hypoalbuminemia
C) Edema
D) Fatty liver
Ans:A
Question 116:A-13-year old boy is referred for evaluation of nocturnal enuresis and short stature. His blood pressure is normal. The hemoglobin level is 8g/dl. Urea 112 mg/dl, creatinine 6 mg/dl, sodium 119 mEq/dl, potassium 4 mEq/l, calcium 7 mg/dl, phophate 6 mg/dl and alkaline phophatase 300 U/l. Urinalysis shows trace proteinuria with hyaline casts; no red and white cells are seen. Ultrasound shows bilateral small kindneys and the micturating cystourethrogram is normal. The most likely diagnosis is ?
A) Alport's syndrome
B) Medullary sponge kidney
C) Chronic glomerulonephritis
D) Nephronophthisis
Ans:D
Question 117:A three years old boy presents with poor urinary stream. Most likely cause is ?
A) Stricture urethra
B) Neurogenic bladder
C) Urethral calculus
D) Posterior urethral valves
Ans:D
Question 118:A newborn infant refuses breast milk since the 2nd day of birth, vomits on force-feeding but accepts glucose-water, develops diarrhoea on the third day, by the 5th day she is jaundiced with liver enlargement and eyes show signs of cataract. Urinary reducing sugar was positive but blood glucose estimated by glucose oxidation method was found low. The most likely cause is deficiency of ?
A) Galactose-1-phosphate uridyl transferase
B) Beta galactosidase
C) Glucose-6-phosphatase
D) Galactokinase
Ans:A
Question 119:A newborn baby has been referred to the casualty as a case of congenital diaphragmatic hernia. The first clinical intervention is of ?
A) Insert a central venous pressure line
B) Bag and mask ventilation
C) Insert a nasogastric tube
D) Ventilate with high frequency ventilator
Ans:C
Question 120:A newborn baby had normal APGAR score at birth and developed excessive frothing and choking on attempted feeds. The investigation of choice is ?
A) Esophagoscopy
B) Bronchoscopy
C) MRI chest
D) Xray chest and abdomen wiht the red rubber catheter passed per orally into oesophagus
Ans:A
Question 121:A drop in fetal heart rate that typically lasts less than 2 minutes and is usually associated with umbilical cord compression is called ?
A) Early deceleration
B) Late deceleration
C) Variable deceleration
D) Prolonged deceleration
Ans:C
Question 122:A 9 yr old boy has steriod dependent nephrotic syndrome for the last 5 years. He had received corticosteroids almost continuously during this period and has cushingoid features. The blood pressure is 120/86 mmHg and there are bilateral subcapsular cataracts. The treatment of choice is ?
A) Levamisole
B) Cyclophosphamide
C) Cyclosporin A
D) Intravenous pulse corticosteriods
Ans:B
Question 123:A 3 year old boy is detected to have bilateral renal calculi. Metabolic evaluation confirms the presence of marked hypercalciuria with normal blood levels of calcium, magnesium, phosphate, uric acid and creatinine. A diagnosis of idiopathic hypercalciuria is made. The dietary management includes all , except ?
A) Increased water intake
B) Low sodium diet
C) Reduced Calcium intake
D) Avoid meat proteins
Ans:C
Question 124:A 11-month old boy, weighing 3 kg, has polyuria, polydipsia and delayed motor milestones. Blood investigations show creatinine of 0.5 mg/dl, potassium 3mEq/L, sodium 125 mEq/L, chloride 88 mEq/L, calcium 8.8 mg/dl, pH 7.46 and bicarbonate 26 mEq/L. Ultrasonography shows medullary nephrocalcinosis. The most likely diagnosis is ?
A) Renal tubular acidosis
B) Diabetes insipidus
C) Bartters syndrome
D) Pseudohypoaldosteronism
Ans:C
A) Atrial septal defect
B) Hypoplastic left heart syndrome
C) Truncus arteriosus
D) Double outlet right ventricle
Ans:A
Question 106:The treatment of choice for primary grade V vesicoureteric reflux involving both kidneys in a 6 month old boy is ?
A) Antibiotic prophylaxis
B) Ureteric reimplantation
C) Cystoscopy followed by subureteric injection of teflon
D) Bilateral ureterostomies
Ans:B
Question 107:The recommended treatment for preputial adhesions producing ballooning of prepuce during micturition in a 2 year old boy is ?
A) Wait and watch policy
B) Circumcision
C) Doral slit
D) Preputial adhesions release and dilatation
Ans:D
Question 108:The narrowest part of larynx in infants is at the cricoid level. In administering anaethesia this may lead to all except ?
A) Choosing a smaller size endotracheal tube
B) Trauma to the subglottic region
C) Post operative stridor
D) Laryngeal oedema
Ans:D
Question 109:The most common leukocytoclastic vasculitis affecting children is ?
A) Takayasu disease
B) Mucocutaneous lymph node syndrome (Kawasaki disease)
C) Henoch Schonlein Purpura
D) Polyarteritis nodosa
Ans:C
Question 110:The following statements regarding Turner syndrome are true except ?
A) Occurrence of Turner syndrome is influenced by maternal age
B) Most patients have primary amenorrhoea
C) Most patients have short stature
D) Edema of hands and feet is an important feature during infancy
Ans:A
Question 111:One year old male child is presented with poor urinary stream since birth. The investigation of choice for evaluation is ?
A) Voiding cystourethrography (VCUG)
B) USG bladder
C) Intravenous urography
D) Uroflometry
Ans:A
Question 112:In neonatal screening programme for detection of congenital hypothyroidismm the ideal place and time to collect the blood sample for TSH estimation is ?
A) Cord blood at time of birth
B) Heal pad blood at the time of birth
C) Heal pad blood on 4 day of birth
D) Peripheral venous blood on 28 day
Ans:A
Question 113:Commonest cause of neonatal mortality in India is ?
A) Diarrheal diseases
B) Birth injuries
C) Low birth weight
D) Congenital anomalies
Ans:C
Question 114:All of the following methods are used for the diagnosis of HIV infection in a 2 month old child, except ?
A) DNA-PCR
B) Viral culture
C) HIV ELISA
D) p24 antigen assay
Ans:C
Question 115:All of the following are characterstic features of Kwashiorkor, except ?
A) High blood osmolarity
B) Hypoalbuminemia
C) Edema
D) Fatty liver
Ans:A
Question 116:A-13-year old boy is referred for evaluation of nocturnal enuresis and short stature. His blood pressure is normal. The hemoglobin level is 8g/dl. Urea 112 mg/dl, creatinine 6 mg/dl, sodium 119 mEq/dl, potassium 4 mEq/l, calcium 7 mg/dl, phophate 6 mg/dl and alkaline phophatase 300 U/l. Urinalysis shows trace proteinuria with hyaline casts; no red and white cells are seen. Ultrasound shows bilateral small kindneys and the micturating cystourethrogram is normal. The most likely diagnosis is ?
A) Alport's syndrome
B) Medullary sponge kidney
C) Chronic glomerulonephritis
D) Nephronophthisis
Ans:D
Question 117:A three years old boy presents with poor urinary stream. Most likely cause is ?
A) Stricture urethra
B) Neurogenic bladder
C) Urethral calculus
D) Posterior urethral valves
Ans:D
Question 118:A newborn infant refuses breast milk since the 2nd day of birth, vomits on force-feeding but accepts glucose-water, develops diarrhoea on the third day, by the 5th day she is jaundiced with liver enlargement and eyes show signs of cataract. Urinary reducing sugar was positive but blood glucose estimated by glucose oxidation method was found low. The most likely cause is deficiency of ?
A) Galactose-1-phosphate uridyl transferase
B) Beta galactosidase
C) Glucose-6-phosphatase
D) Galactokinase
Ans:A
Question 119:A newborn baby has been referred to the casualty as a case of congenital diaphragmatic hernia. The first clinical intervention is of ?
A) Insert a central venous pressure line
B) Bag and mask ventilation
C) Insert a nasogastric tube
D) Ventilate with high frequency ventilator
Ans:C
Question 120:A newborn baby had normal APGAR score at birth and developed excessive frothing and choking on attempted feeds. The investigation of choice is ?
A) Esophagoscopy
B) Bronchoscopy
C) MRI chest
D) Xray chest and abdomen wiht the red rubber catheter passed per orally into oesophagus
Ans:A
Question 121:A drop in fetal heart rate that typically lasts less than 2 minutes and is usually associated with umbilical cord compression is called ?
A) Early deceleration
B) Late deceleration
C) Variable deceleration
D) Prolonged deceleration
Ans:C
Question 122:A 9 yr old boy has steriod dependent nephrotic syndrome for the last 5 years. He had received corticosteroids almost continuously during this period and has cushingoid features. The blood pressure is 120/86 mmHg and there are bilateral subcapsular cataracts. The treatment of choice is ?
A) Levamisole
B) Cyclophosphamide
C) Cyclosporin A
D) Intravenous pulse corticosteriods
Ans:B
Question 123:A 3 year old boy is detected to have bilateral renal calculi. Metabolic evaluation confirms the presence of marked hypercalciuria with normal blood levels of calcium, magnesium, phosphate, uric acid and creatinine. A diagnosis of idiopathic hypercalciuria is made. The dietary management includes all , except ?
A) Increased water intake
B) Low sodium diet
C) Reduced Calcium intake
D) Avoid meat proteins
Ans:C
Question 124:A 11-month old boy, weighing 3 kg, has polyuria, polydipsia and delayed motor milestones. Blood investigations show creatinine of 0.5 mg/dl, potassium 3mEq/L, sodium 125 mEq/L, chloride 88 mEq/L, calcium 8.8 mg/dl, pH 7.46 and bicarbonate 26 mEq/L. Ultrasonography shows medullary nephrocalcinosis. The most likely diagnosis is ?
A) Renal tubular acidosis
B) Diabetes insipidus
C) Bartters syndrome
D) Pseudohypoaldosteronism
Ans:C
